Journal of Mahatma Gandhi Institute of Medical Sciences

CASE REPORT
Year
: 2018  |  Volume : 23  |  Issue : 2  |  Page : 92--94

Syndrome of right isomerism: Ivemark syndrome


Dipti Jain1, Bhushan Chavan2, Anita Manoj1 
1 Department of Pediatrics, Dr. BAM Hospital, Mumbai, Maharashtra, India
2 Department of Pediatric Cardiology, Dr. BAM Hospital, Mumbai, Maharashtra, India

Correspondence Address:
Dr. Dipti Jain
C/7, Nirmal Park, Byculla East, Mumbai - 400 047, Maharashtra
India

Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidity and mortality. Abnormal cardiac development typically leads to atrial appendage isomerism, resulting in either bilateral paired right atria (right atrial isomerism or paired left atria (left atrial isomerism. Here we present a one and a half-month-old female child with right isomerism.


How to cite this article:
Jain D, Chavan B, Manoj A. Syndrome of right isomerism: Ivemark syndrome.J Mahatma Gandhi Inst Med Sci 2018;23:92-94


How to cite this URL:
Jain D, Chavan B, Manoj A. Syndrome of right isomerism: Ivemark syndrome. J Mahatma Gandhi Inst Med Sci [serial online] 2018 [cited 2022 Dec 5 ];23:92-94
Available from: https://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=Jain;type=0